Marfan Syndrome: Prevalence of Aortic Dissection and Postoperative Outcomes in a referral hospital in Mexico

Presented During:

Thursday, April 25, 2024: 5:38PM - 7:00PM
Sheraton Times Square  
Posted Room Name: Central Park  

Abstract No:

P0210 

Submission Type:

Abstract Submission 

Authors:

Jesus Sanchez Pacheco (1), Benjamin Ivan Hernandez Mejia (2), Humberto Jorge Martinez Hernandez (2), María Elena Soto López (2)

Institutions:

(1) N/A, N/A, (2) Instituto Nacional de Cardiología Ignacio Chávez, Mexico City, NA

Submitting Author:

Jesus Sanchez Pacheco    -  Contact Me
N/A

Co-Author(s):

Benjamin Ivan Hernandez Mejia    -  Contact Me
Instituto Nacional de Cardiología Ignacio Chávez
Humberto Jorge Martinez Hernandez    -  Contact Me
Instituto Nacional de Cardiología Ignacio Chávez
María Elena Soto López    -  Contact Me
Instituto Nacional de Cardiología Ignacio Chávez

Presenting Author:

Jesus Sanchez Pacheco    -  Contact Me
N/A

Abstract:

Objective: Describe the characteristics and postoperative outcomes of patients with Marfan syndrome and aortic dissection in a referral hospital in Mexico.

Methods: retrospective study during the period from January 1, 2012 to March 31, 2022.

Results: We identified 74 patients with Marfan syndrome and similar pathologies who underwent surgery; 64 patients met more than two Ghent criteria for Marfan syndrome and 28 of them presented aortic dissection with a prevalence of 4.78%. Aneurysmal dilatation of the ascending aorta was present in 78% of patients with Marfan syndrome, aortic dissection in 44%(28). Acute aortic dissection was the most frequent type of dissection with 17%. The mean age at the time of dissection was 22 ± 3 years. The most frequently performed surgery was Bentall and de Bono in 22 of the patients. Complications occurred in 18 patients with aortic dissection. In-hospital death occurred in 11%.

Conclusions: The high mortality of aortic dissection demands for early diagnosis and comprehensive atention to assess the need for prophylactic intervention.
Working in new strategies for timely diagnosis, screening and decision-making pathways that lead to excellence in the care of patients with Marfan Syndrome is needed for the improvement of outcomes

Aortic Symposium:

Dissection

 

Keywords - Adult

Aorta - Aortic Disection